Hallervorden-spatz syndrome

A rare hereditary, degenerative neurological disease, whose onset usually is before adolescence. Symptoms include dystonia, spasticity, and a gradually progressive dementia.


Hallervorden-Spatz disease (HSD) is a rare, progressive, neurological movement disorder characterized by extrapyramidal and pyramidal motor symptoms, mental deterioration, and abnormally high deposits of iron in the brain. It is an inherited autosomal recessive disorder and has been reported in both males and females. Incidence data was not available in the literature.


A degenerative neurological disorder found in children; characterized by parkinsonism, rigidity, and progressive dementia due to accumulation of iron pigments in the brain.


 


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