Ichthyosis congenita

Ichthyosis congenita is an inherited skin disorder characterized by generalized dry and rough skin. All babies who suffer from an autosomal recessive congenita ichthyosis are collodion babies at birth. Collodion babies are born with a translucent or opaque membrane that covers the entire body and lasts for days to weeks. Congenita ichthyosis presents on a spectrum in which lamellar ichthyosis is the most severe and non bullous congenital ichthyosis is a mild form of congenita ichthyosis. In lamellar ichthyosis the collodion membrane is replaced by dark brown plate like scales without erythroderma (abnormal redness of the skin). The non bullous type presents with erythroderma with fine white scales.


 


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