1.0Glossaryhttps://www.healthbenefitstimes.com/glossaryGlossaryhttps://www.healthbenefitstimes.com/glossary/author/adminglossary/Schwachman syndrome - Definition of Schwachman syndromerich600338<blockquote class="wp-embedded-content" data-secret="Nv3uvUcyaA"><a href="https://www.healthbenefitstimes.com/glossary/schwachman-syndrome/">Schwachman syndrome</a></blockquote><iframe sandbox="allow-scripts" security="restricted" src="https://www.healthbenefitstimes.com/glossary/schwachman-syndrome/embed/#?secret=Nv3uvUcyaA" width="600" height="338" title="“Schwachman syndrome” — Glossary" data-secret="Nv3uvUcyaA" frameborder="0" marginwidth="0" marginheight="0" scrolling="no" class="wp-embedded-content"></iframe><script>
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Schwachman syndrome (SS) is a rare, heritable disorder consisting of pancreatic insufficiency (inadequate amounts of pancreatic digestive enzymes), neutropenia (decreased number of neutrophils, a type of white blood cell), defects in neutrophil function, anomalous bone formation, postnatal growth retardation with poor weight gain (failure to thrive), and short stature. Patients are usually normal at birth but soon develop steatorrhea (greasy, foul-smelling stools secondary to fat malabsorption caused by pancreatic enzyme deficiency) and growth failure.