{"id":107731,"date":"2021-05-23T04:33:23","date_gmt":"2021-05-23T04:33:23","guid":{"rendered":"https:\/\/www.healthbenefitstimes.com\/glossary\/?p=107731"},"modified":"2021-05-27T04:55:02","modified_gmt":"2021-05-27T04:55:02","slug":"von-gierkes-disease","status":"publish","type":"post","link":"https:\/\/www.healthbenefitstimes.com\/glossary\/von-gierkes-disease\/","title":{"rendered":"Von gierke’s disease"},"content":{"rendered":"

A rare genetic disorder characterized by excess glycogen stores in liver and muscles due to a mutation in the gene for the enzyme glucose-6-phosphatase. Also called type I glycogen storage disease.<\/p>\n

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Von Gierke disease is an inherited disorder caused by an inborn lack of the enzyme glucose-6-phosphatase (G6Pase). G6Pase is critical for its role in the liver\u2019s production of glucose, which the body uses for energy. When G6Pase is missing, glycogen accumulates in the liver, kidneys, and – intestines. Von Gierke disease is one type of glycogen storage disease (GSD); there are about 11 known types altogether. Von Gierke disease may also be referred to as glycogen storage disease la, glycogenosis Type I, and hepatorenal glycogenosis.<\/p>\n

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 <\/p>\n","protected":false},"excerpt":{"rendered":"

A rare genetic disorder characterized by excess glycogen stores in liver and muscles due to a mutation in the gene for the enzyme glucose-6-phosphatase. Also called type I glycogen storage disease. Von Gierke disease is an inherited disorder caused by an inborn lack of the enzyme glucose-6-phosphatase (G6Pase). G6Pase is critical for its role in […]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[22],"tags":[],"class_list":["post-107731","post","type-post","status-publish","format-standard","hentry","category-v"],"yoast_head":"\nVon gierke's disease - Definition of Von gierke's disease<\/title>\n<meta name=\"description\" content=\"A rare genetic disorder characterized by excess glycogen stores in liver and muscles due to a mutation in the gene for the enzyme glucose-6-phosphatase. Also called type I glycogen storage disease.Von Gierke disease is an inherited disorder caused by an inborn lack of the enzyme glucose-6-phosphatase (G6Pase). G6Pase is critical for its role in the liver\u2019s production of glucose, which the body uses for energy. When G6Pase is missing, glycogen accumulates in the liver, kidneys, and - intestines. Von Gierke disease is one type of glycogen storage disease (GSD); there are about 11 known types altogether. Von Gierke disease may also be referred to as glycogen storage disease la, glycogenosis Type I, and hepatorenal glycogenosis.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.healthbenefitstimes.com\/glossary\/von-gierkes-disease\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Von gierke's disease - Definition of Von gierke's disease\" \/>\n<meta property=\"og:description\" content=\"A rare genetic disorder characterized by excess glycogen stores in liver and muscles due to a mutation in the gene for the enzyme glucose-6-phosphatase. Also called type I glycogen storage disease.Von Gierke disease is an inherited disorder caused by an inborn lack of the enzyme glucose-6-phosphatase (G6Pase). G6Pase is critical for its role in the liver\u2019s production of glucose, which the body uses for energy. When G6Pase is missing, glycogen accumulates in the liver, kidneys, and - intestines. Von Gierke disease is one type of glycogen storage disease (GSD); there are about 11 known types altogether. Von Gierke disease may also be referred to as glycogen storage disease la, glycogenosis Type I, and hepatorenal glycogenosis.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.healthbenefitstimes.com\/glossary\/von-gierkes-disease\/\" \/>\n<meta property=\"og:site_name\" content=\"Glossary\" \/>\n<meta property=\"article:published_time\" content=\"2021-05-23T04:33:23+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2021-05-27T04:55:02+00:00\" \/>\n<meta name=\"author\" content=\"Glossary\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Written by\" \/>\n\t<meta name=\"twitter:data1\" content=\"Glossary\" \/>\n\t<meta name=\"twitter:label2\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data2\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/www.healthbenefitstimes.com\/glossary\/von-gierkes-disease\/\",\"url\":\"https:\/\/www.healthbenefitstimes.com\/glossary\/von-gierkes-disease\/\",\"name\":\"Von gierke's disease - Definition of Von gierke's disease\",\"isPartOf\":{\"@id\":\"https:\/\/www.healthbenefitstimes.com\/glossary\/#website\"},\"datePublished\":\"2021-05-23T04:33:23+00:00\",\"dateModified\":\"2021-05-27T04:55:02+00:00\",\"author\":{\"@id\":\"https:\/\/www.healthbenefitstimes.com\/glossary\/#\/schema\/person\/ccfef987a4882e6356ae6d77d33e74c5\"},\"description\":\"A rare genetic disorder characterized by excess glycogen stores in liver and muscles due to a mutation in the gene for the enzyme glucose-6-phosphatase. 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